Abstract
Double aortic arch is one of the rarest congenital anomalies, associated with the embryonic persistence of
the right 4th aortic arch. More often than other variants of vascular rings, this defect causes symptoms of
compression of the esophagus and trachea. We present a case of a rare form of a double arch of the aorta with
codominant arches, forming a vascular ring around the trachea and esophagus in newborn. This anomaly was
suspected prenatally during fetal echocardiography and has been confirmed by multispiral computed tomography
data. The operation of vascular ring dissociation after an accurate diagnosis has been carried out in
order to prevent not only the early manifestations and complications of this anomaly, but also a pathological
process like tracheobronchomalacia in the long term. Timely early surgical treatment of a double aortic arch
makes the prognosis favorable.
References
-
Park M.K. Vascular Rings. In: Park M.K. (Ed.) Pediatric
cardiology for practitioners. 4th edn, St. Louis: Mosby;
2012: 241.
- Asenaidi K., Gurofsky R., Karmlou T., Williams W.G.,
McCrindle B.W. Management and outcome of double
aortic arch in 81 patients. Pediatrics. 2006; 118 (5):
e1336–41.
DOI: 10.1542/peds.2006-1097
- Edwards F.R. Vascular compression of the trachea and
esophagus. Thorax. 1959; 14 (3): 187–200.
DOI:
10.1136/thx.14.3.187
- Ekström G., Sandblom P. Double aortic arch. Acta Chir.
Scand. 1951; 102 (3): 183–202.
- McFaul R., Millard P., Nowicki E. Vascular rings
necessitating right thoracotomy. J. Thorac. Cardiovasc.
Surg. 1981; 82 (2): 306–39.
- Holmes K.W., Bluemke D.A., Vricella L.A., Ravekes
W.J., Kling K.M., Spevak P.J. Magnetic resonance
imaging of distorted left subclavian artery course: an
important clue to an unusual type of aortic arch.
Pediatr. Cardiol. 2006; 27(3): 316–20.
DOI:10.1007/s00246-005-1118-x
- Gross R. Thoracic surgery for infants. J. Thorac.
Cardiovasc. Surg. 1964; 48: 229–309.
- Chan Y.T., Ng D., Chong A.S.F., Ho J. Double aortic
arch presenting as neonatal stridor. J. Paediatr. 2003; 8:
126–9.
- Abdelhafid H., Mustapha B., Redouane A., Badr S.,
Hicham B., Salim Jaafar Lalaoui. Double aortic arch
presenting with respiratory distress: A case report and
review of the literature. Saudi J. Anaesth. 2017; 11 (4):
483–5.
DOI: 10.4103/sja.SJA_249_17
- Torre M., Carlucci M., Speggiorin S., Elliott M.J.
Aortopexy for the treatment of tracheomalacia in children:
review of the literature. It. J. Pediatr. 2012; 38: 62.
DOI: 10.1186/1824-7288-38-62
- Aysel T., Fatma G., Turhan C., Tülay Ö. Congenital
anomalies of the aortic arch: evaluation with the use of
multidetector computed tomography. Korean J. Radiol.
2009; 10 (2): 176–84. DOI: 10.3348/kjr.2009.10.2.176
- Etesami M., Ashwath R., Kanne J., Gilkeson R.C.,
Rajiah P. Computed tomography in the evaluation of
vascular rings and slings. Insights Imaging. 2014; 4:
507–21.
DOI: 10.1007/s13244-014-0343-3.
About the authors
- Rasumovskiy Vadim Sergeevich, Postgraduate; orcid.org/0000-0001-7802-4588
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Svobodov Andrey Andreevich, Dr. Med. Sc., Chief Researcher; orcid.org/0000-0003-2523-5212
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Gulasaryan Ruben Sergeevich, Cand. Med. Sc., Senior Researcher; orcid.org/0000-0001-7664-8506
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Levchenko Elena Grigor’evna, Cand. Med. Sc., Senior Researcher
