Abstract
Pulmonary atresia (PA) is a rare congenital heart disease which accounts for about 2–3% of all congenital
heart diseases cases in children. This category of patients belongs to one of the most difficult due to the large
anatomical variety of this disease. The tactic of surgical treatment is still a subject of discussion around the
world, and no clinic has ever been able to find answer to it. In this article, we present the tactics of managing
a patient 11 month old with type 2 PA with ventricular septal defect and major aorto-pulmonary collaterals
with a description of the technical aspects of the performed operation.
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About the authors
- Shcherbak Anastasiya Vital'evna, Cardiovascular Surgeon; orcid.org/0000-0002-0723-9028
-
Zelenikin Mikhail Mikhailovich, Dr. Med. Sc., Professor, Head of Department; orcid.org/0000-0002-1298-2940
-
Volkov Sergey Sergeevich, Cand. Med. Sc., Senior Researcher, Cardiovascular Surgeon; orcid.org/0000-0003-2005-4957
-
Dibin Denis Andreevich, Anesthesiologist-Resuscitator; orcid.org/0000-0003-1194-2688