Abstract
Atrioventricular canal (AVC) is a defect with progressive course. Therefore its early diagnosis and
settlement of the problem of surgical treatment are essential. The choice of surgical approach for
atrioventricular valve (AV) correction in infants with full AVC form is a relevant problem today.
Many surgeons describe improvement of surgical correction results with complete AVC form and
reduction of surgical lethality rate during the latest decade.
The most often late complication following radical correction of atrioventricular canal is development
and progression of the left atrioventricular valve incompetence. Moderate or highgrade
regurgitation of atrioventricular valve in the late postoperative period was noted in 5-23%
patients with complete form of AVC.
The situations in which reconstructive manipulations on the mitral valve (MV) during the primary
correction will not result in complete elimination of mitral insufficiency.
1. Fibrous and/or myxomatous degeneration of the MV leaflets and chordal papillar apparatus.
2. Short MV chordae originating from the left ventricle walls.
3. Agenesis, hypoplasia or marked malformation of one of the MV leaflets.
4. Marked multicomponent insufficiency of MV with potentially parachute-shaped double
MV.
MV replacement is preferable in all these cases. Important reason of the intact MV plasty impossibility
is the absence or lack of skills of the operating surgeon to accomplish various techniques
of valvular reconstruction. Most authors aiming to preserve MV during the primary correction
of AVC point to this.
A number of questions come up following the analysis of the literature dedicated to surgical
treatment for (CFAVC) and in particular correction of valvular malformation associated
with this pathology. Should we accomplish MV replacement in the early age or would it be
enough to perform reconstructive surgery even if it is less hemodynamically efficient? If an
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