Abstract
The article has generalized the worlds experience in diagnostic and surgical treatment of the anomalous origin of the left pulmonary
artery from the ascending aorta as well as the congenital heart diseases associated with this pathology.
Anomalous origin of the left pulmonary artery from the ascending aorta is a rare congenital disease of the truncus which is characterized
by systemic blood supply of the ipsilateral lung from the pulmonary artery originating from the ascending aorta in the condition of the normal
blood supply of the other lung from the contralateral pulmonary artery originating from the pulmonary trunk.
84 cases were reported in the available world literature regarding the anomalous origin of the left pulmonary artery from the ascending
aorta.14 % (n = 12) reported the isolated form, 86 % (n = 72) reported the pathology associated with other congenital diseases of the cardiovascular
system. 55 (76 %) out of 72 cases reported the anomalous origin of the left pulmonary artery from the ascending aorta associated
with congenital heart diseases and decreased circulation in the contralateral (right) lung, 17 (24 %) reported association with
congenital heart diseases and increased pulmonary circulation. The age median of patients with the anomalous origin of the left pulmonary
artery from the ascending aorta at the first admission has made up 1 year.
Unfavourable prognosis in the condition of natural development of the anomalous origin of the left pulmonary artery from the ascending
aorta is concomitant with development of the pulmonary hypertension leading to the heart failure in early childhood.
The recent modes of examination of patients allow identifying in ones life time the anomalous origin of the left pulmonary artery from
the ascending aorta. Diagnostics of this anomaly include echocardiography, angiocardiography, multispiral computed and magnetic resonance
tomography.
The optimal method of surgical correction of this anomaly is the re-implantation of the anomalously originating from the ascending
aorta pulmonary artery into the pulmonary trunk and with the availability of associated intracardiac defects the elimination of such.
The world experience of surgical treatment of patients with the anomalous origin of the left pulmonary artery from the ascending aorta
reported 64 cases with hospital mortality of 16 % (n = 10).
